NRS 434V Group PP Week 4 1 essay

NRS 434V Group PP Week 4 1 essay

Clinical Description and Definition of
the Disease.
“Cystic Fibrosis is a life threatening, genetic disease that causes persistent lung infections, and progressively limits the ability to breathe” (“Cystic Fibrosis,” n.d.).

Pathophysiology and
History of
the Disease
• Cystic Fibrosis is caused by defects in
the cystic fibrosis gene.
• Cystic Fibrosis was recognized over 400
years ago in Germany.
• There is no cure for Cystic Fibrosis.

Impact on Adults to the Health
Care System and Nursing Practice
• Increased heath care costs
• Over crowed clinics
• Individuals received less personal
attention
• Limited number of hospital beds
• Nursing education

Impact of the Disease on Childhood

• Altered body image
• Impaired relationship with peers
• Impact of living with a chronic disease

Impact of the Disease on Adults
• Burden of care increases
• Taking more medicines and receiving
more treatments.
• Lung damage is greater in adulthood
than earlier in life.
• Fertility issues (Heintz, 2010, para. 6)

Reasons People with CF are
living into Adulthood
• GENE THERAPY
• ANTIMICROBIAL THERAPY
• THE MODERN CF CARE
CENTER
• MUCOLYTICS
• MUCOCILIARY CLEARANCE

Impacts this Disease will have
on the Adult Client.
• Mentally and emotionally
• Physically
• Sexually
• Economically, specifically as it relates to the ability to access health insurance and health care
• Susceptibility to engage in substance abuse
• Prenatal care and childbearing (see additional slide)
• Occupational considerations and hazards (see additional slide) • Ability to cope with stress (see additional slide)

Pregnancy
Pregnancy
is now
possible
with cystic
fibrosis

Pregnancy
• Importance of Prenatal Care
• Pregnancy Statistics
• Focus on Family Planning

Infertility causes
• The majority of men
with cystic fibrosis
have associated
congenital bilateral
absence of the vas
deferens ( mutations,
1995).

• Female infertility is
less clear. There is
a theory that the
vaginal mucosa is to
thick for sperm
passage. Other
reasons are thought
to be low BMI, poor
nutrition, and
chronic infection
(Hodges, 2008).

Choosing a career
• Cystic Fibrosis should not
prevent one from pursuing the
career they seek
• Some careers pose greater
health risks for Cystic Fibrosis
patients
(Careers, 2013)

Learning to cope
The key is to limit stress by:
– Knowledge: ask, watch, study and read
– Support: support groups, get in touch with other families that know the ropes.
– Planning: getting through daily life will be overwhelming, write a daily plan.
– Strength: do not listen to well meaning people with
negative advise listen to your healthcare providers
(About, 2014).

Outcomes for the Adult Patient
• Adequate airway clearance
• Reduction of risk factors associated with
respiratory infections